Hailey – Hailey disease: A case report
Keywords:
Hailey, Halley disease, chronic benign family pemphigus, genodermatoid, suprabasal acantholysisAbstract
Hailey – Hailey disease, is described for the first time in 1939 by Hailey brothers. It is a chronic autosomic dominant dermatitis that generally has a benign course. The diagnosis is clinical, biopsy should be performed to confirm it; if its chronicity, recurrence and limited therapeutics options are taken into considerations, it represents a challenge, because there is not any healing treatment. This information is presented with the objective to show the importance of the early diagnosis to improve the life quality of patients. A 72-year-old male white patient, with personal history of grade II essential hypertension, ischemic cardiopathy and diabetes mellitus type II, went to the consultation complaining of bothering, uncomfortable, fetid, pruritic and sometimes painful skin lesions. Its diagnosis and multidisciplinary follow-up treatment are important since early ages, these aspects allow to perform an adequate medical advice to the families.
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